Carney triad
It is the
combination of a gastric tumor (leiomyoblastoma which is a tumor of smooth
muscle cells formed embryonic appearance) to an extra-adrenal paraganglioma
(see pheochromocytoma) and pulmonary chondroma. (Benign cartilage)
Its cause is
still unknown.
This could be
related to a disorder of embryonic development of the NEURAL CREST (see this
term).
This syndrome
has been noted among young women,
around thirty,
generally blood group.
The evolution of
the disease is slow and has most often decades.
SYMPTOMS
At first they
are gastrointestinal bleeding manifested,
and
complications of paraganglioma at the end of evolution (metastatic tumor
progression, accidents crisis hypertension).
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